What is the formula for PKU?

Phenyl-Free 1 is an iron-fortified infant formula & medical food powder that is free of the essential amino acid phenylalanine. It is specially designed for infants and toddlers with phenylketonuria (PKU).

How do you test for PKU?

The blood sample for PKU is usually taken from your baby’s heel (called a heel stick). The test is done in the first few days after birth, as early as 24 hours after birth. The test may be repeated within the first week or two after birth.

What is Lofenalac formula?

Lofenalac (pronunciation:Lo-fen-alac) is a registered, trademarked infant powder formula prescribed to replace milk in the diets of phenylketonuria sufferers in the infant and child stage. It is not recommended for non-PKU patients. In 1972, Lofenalac was declared a food by the FDA, for regulatory purposes.

What can Babies with PKU eat?

A child with PKU should not eat milk, fish, cheese, nuts, beans, or meat. A child with PKU can eat many foods low in protein, such as vegetables, fruits, and some cereals. Your child may also need to take mineral and vitamin supplements to make up for nutrients missing from the diet.

When is 2nd PKU test done?

The American Academy of Pediatrics recommends that a PKU screening test be repeated by two weeks of age if it was performed before the newborn was 24 hours of age.

What is CCHD screening?

To screen for CCHD, a doctor or nurse uses a device called a pulse oximeter. The device has a sensor that attaches to a baby’s right hand and either foot. It shines light through the skin to measure oxygen in the blood. The screening process is painless and happens at the bedside or in the nursery.

What is the so called Guthrie test based on?

The Guthrie test, also called the PKU test, is a diagnostic tool to test infants for phenylketonuria a few days after birth. To administer the Guthrie test, doctors use Guthrie cards to collect capillary blood from an infant’s heel, and the cards are saved for later testing.

What foods should you avoid if you have PKU?

PKU diets typically do not contain high-protein foods such as:

Meat, eggs, and fish.
Bread, noodles, and wheat products.
Nuts, peas, and beans (and products made from these foods).
Milk and cheese.
Chocolate.

Can you grow out of PKU?

A person with PKU does not outgrow it and must stay on the diet for life.

What do PKU babies drink?

If your baby has PKU, what kind of treatment do they need?

Milk, cheese, ice cream and other dairy products.
Eggs.
Meat and poultry.
Fish.
Nuts, seeds, oats, rye, barley, gelatin.
Beans.
Food or drinks that contain aspartame. This is an artificial sweetener that has a lot of phenylalanine in it.

What is a positive PKU test?

Ask the healthcare provider what the test results mean for your child. The test screens for blood levels of phenylalanine. Normal levels of phenylalanine in the blood are less than 2 milligrams per deciliter (mg/dL). More than 4 mg/dL of phenylalanine in the blood is considered high and may mean your child has PKU.